Noncompaction cardiomyopathy

Non-compaction cardiomyopathy (NVM) is a structural malformation of the ventricular myocardium of unknown etiology, often associated with genetic diseases such as neuromuscular disorders and chromosomal defects. It is a rare congenital heart disease. Based on whether it is accompanied by other diseases, it can be divided into two types: Isolated non-compaction cardiomyopathy: not accompanied by cardiac malformations Non-compaction cardiomyopathy accompanied by other congenital heart diseases Based on the location of the lesion, it can also be divided into three types: Left ventricular type: highest incidence Right ventricular type Biventricular type This disease is more common in children, and the incidence in adults is higher than expected. In the early stage, there may be no specific clinical manifestations. Patients often experience exertional dyspnea, lower limb edema, chest pain, palpitations, and other discomforts due to complications such as heart failure, thromboembolism, or ventricular arrhythmias. In severe cases, syncope, coma, or even sudden cardiac death may occur.